{"created":"2023-06-19T07:39:06.681166+00:00","id":2765,"links":{},"metadata":{"_buckets":{"deposit":"0ba88a12-f9a0-406d-afbf-73ad4d50523a"},"_deposit":{"created_by":3,"id":"2765","owners":[3],"pid":{"revision_id":0,"type":"depid","value":"2765"},"status":"published"},"_oai":{"id":"oai:mdu.repo.nii.ac.jp:00002765","sets":["178:307","193:201:451","193:208:288"]},"author_link":["4431","4428","4430","4425","4432","4426","4423","4427","4429","4433","4422","4424"],"item_7_biblio_info_7":{"attribute_name":"書誌情報","attribute_value_mlt":[{"bibliographicIssueDates":{"bibliographicIssueDate":"1987-03","bibliographicIssueDateType":"Issued"},"bibliographicIssueNumber":"1","bibliographicPageEnd":"183","bibliographicPageStart":"174","bibliographicVolumeNumber":"25","bibliographic_titles":[{"bibliographic_title":"小児歯科学雑誌"},{"bibliographic_title":"The Japanese Journal of Pediatric Dentistry","bibliographic_titleLang":"en"}]}]},"item_7_description_19":{"attribute_name":"フォーマット","attribute_value_mlt":[{"subitem_description":"application/pdf","subitem_description_type":"Other"}]},"item_7_description_5":{"attribute_name":"抄録","attribute_value_mlt":[{"subitem_description":"先天性赤芽球癆(Josephs-Blackfan-Diamond type) と免疫不全症候群とを合併したきわめて稀な症例に対して,齲蝕治療とその後の歯科的健康管理を行った。初診時は8歳で,生後3ヵ月以降,現在まで切れ目なく副腎皮質ホルモン剤を服用しており,精神発達遅滞と著しい発育障害が認められた。液血液検査では, 血色素量1 3. 6 g / d l , ヘマトクリット4 1 % で, 貧血状態は改善されていたが, 免疫グロブリンは全クラスとも測定可能量を認めなかった。O K T 3 は9 0 % , O K T 4は35.4%,OKT8は52.2%で,cytotoxic/suppressor T cellが優位であった。初診時の主訴は,下顎右側第一大臼歯の感染に起因する自発痛で,他にも治療を要する齲蝕が6歯あった。口腔清掃状態は不良であったが,歯肉および口腔粘膜には著しい病変は認められなかった。精神発達遅滞による不協力が著しかったので,全身麻酔下にて齲蝕治療を行った。その後は,リコール・システムにより歯科的健康管理を行い,良好な経過をみている。1年5ヵ月後(9歳10ヵ月)の側貌頭部X線規格写真では,上下顎前歯の歯軸傾斜に関しては,異常が認められなかったが,骨格的には上下顎の劣成長が認められた。手および手根骨X線写真では,骨成熟度の著しい遅れを認めた。1年8ヵ月後(10歳1ヵ月)に行った模型分析の結果,上下顎とも歯列弓幅径は小さい値を示していた。上下顎の劣成長と骨成熟度の遅延には,副腎皮質ホルモン剤の副作用も関与しているものと考えられた。","subitem_description_type":"Abstract"}]},"item_7_publisher_8":{"attribute_name":"出版者","attribute_value_mlt":[{"subitem_publisher":"(公社)日本小児歯科学会"}]},"item_7_relation_11":{"attribute_name":"NII論文ID","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"130004723361","subitem_relation_type_select":"NAID"}}]},"item_7_relation_13":{"attribute_name":"医中誌ID","attribute_value_mlt":[{"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"1988089484","subitem_relation_type_select":"ICHUSHI"}}]},"item_7_relation_14":{"attribute_name":"DOI","attribute_value_mlt":[{"subitem_relation_name":[{"subitem_relation_name_text":"info:doi/10.11411/jspd1963.25.1_174"}],"subitem_relation_type":"isIdenticalTo","subitem_relation_type_id":{"subitem_relation_type_id_text":"https://doi.org/10.11411/jspd1963.25.1_174","subitem_relation_type_select":"DOI"}}]},"item_7_relation_16":{"attribute_name":"情報源","attribute_value_mlt":[{"subitem_relation_name":[{"subitem_relation_name_text":"雑誌掲載論文(電子版) 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のため,副腎皮質ホルモン剤を長期服用している免疫不全症候群の一例","item_titles":{"attribute_name":"タイトル","attribute_value_mlt":[{"subitem_title":"先天性赤芽球癆(Josephs-Blackfan-Diamond type) のため,副腎皮質ホルモン剤を長期服用している免疫不全症候群の一例"},{"subitem_title":"A case report of constitutional erythroid hypoplasia (Josephs-Blackfan-Diamond Type) with immunodeficiency].","subitem_title_language":"en"}]},"item_type_id":"7","owner":"3","path":["288","307","451"],"pubdate":{"attribute_name":"公開日","attribute_value":"2018-11-15"},"publish_date":"2018-11-15","publish_status":"0","recid":"2765","relation_version_is_last":true,"title":["先天性赤芽球癆(Josephs-Blackfan-Diamond type) のため,副腎皮質ホルモン剤を長期服用している免疫不全症候群の一例"],"weko_creator_id":"3","weko_shared_id":3},"updated":"2023-06-19T07:57:18.447530+00:00"}